| Death of a Severe Underweight Infant with Pulmonary Interstitial Glycogenosis. |
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Seon Jung Jang, Kyung Ryoul Kim, Hyoung Joong Kim, Minjung Kim |
1Division of Forensic Medicine, National Forensic Service, Seoul, Korea. lillu79@korea.kr
2Department of Forensic Medicine, Korea University College of Medicine, Seoul, Korea. |
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| Abstract |
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Pulmonary interstitial glycogenosis (PIG) is a very rare interstitial lung disease in infants. It is poorly understood, but its pathological features are distinct; they include uniform alveolar septal thickening, caused by a group of oval to spindle-shaped cells containing abundant glycogen, without apparent inflammation or fibrosis. PIG is usually associated with a good prognosis. However, in the present report, we describe the case of a 5-month-old male infant who died due to PIG; he was severely underweight and not administered proper treatment or care. The pathology of PIG was determined following a medico-legal autopsy. |
| Key Words:
infant, pulmonary interstitial glycogenosis, underweight, death |
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